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Objective To summarize and discuss my institutes line relatives of the donor , living donor liver transplantation in the treatment of Wilson's degeneration effect and surgical treatment experience to further guide clinical work . Methods From January 2005 to February 2008 , our hospital completed a total of three cases of relatives living donor liver transplantation in the treatment of Wilson variability , patients are children , patients with nervous system dysfunction . The donor liver in two cases the patient 's father , were the mother , ceruloplasmin were normal , 24 - h urinary copper < 100g . Purposes of surgical procedures: three cases are situ part piggyback liver transplantation , the graft is left liver . The results were followed , all donor survival ; subject embodies survived two cases , perioperative death cases cause of death in the portal vein thrombosis and liver poor venous return , and finally died of liver failure . Cases of mixed neurological manifestations mainly patients after elevated bilirubin , balloon dilation of anastomotic three intervention , rapid decline in bilirubin , liver function returned to normal . The patients are still alive , and significant improvement in extrapyramidal symptoms and language and movement disorders . Without patients occurred rejection . Conclusion living donor liver transplantation a correctable pediatric liver degeneration , liver disease and the original metabolic defects , and improve the quality of life of children , to save his life . Is an effective method for the treatment of the pediatric liver degeneration end-stage liver disease . Associated with nervous system dysfunction in patients after the vast majority have varying degrees of improvement .
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